바로가기메뉴

본문 바로가기 주메뉴 바로가기

Tuberculosis & Respiratory Diseases

Article Contents

Prev Next
e-Submission

Vol.71 No.2
Citation Share

Isolated Right Pulmonary Artery Hypoplasia with Retrograde Blood Flow in a 68-Year Old Man

Tuberculosis & Respiratory Diseases / Tuberculosis & Respiratory Diseases,
2011, v.71 no.2, pp.126-133
Youjin Chang (University of Ulsan)





Shin Na (University of Ulsan)
Joo Hee Kim (University of Ulsan)
Tai Sun Park (University of Ulsan)
Soo-Kyung Park (University of Ulsan)
Seong Joon Park (University of Ulsan)
Taehoon Lee (University of Ulsan)
Young-Chel Ahn (University of Ulsan)
Youjin, C. , Shin, N. , Joo, H. K. , Tai, S. P. , Soo-Kyung, P. , Seong, J. P. , Taehoon, L. , & Young-Chel, A. (2011). Isolated Right Pulmonary Artery Hypoplasia with Retrograde Blood Flow in a 68-Year Old Man. Tuberculosis & Respiratory Diseases, 71(2), 126-133.
  • Downloaded
  • Viewed
PDF Download

Abstract

Unilateral pulmonary artery hypoplasia (UPAH) is a rare disease in adults and is frequently accompanied by a congenital cardiac anomaly at a young age. The diagnosis is usually based on computed tomography (CT), angiography, and magnetic resonance imaging (MRI). However, no reports are available on retrograde flow in patients with UPAH. We describe a 68-year-old man with isolated UPAH and retrograde blood flow. He was admitted for dyspnea on exertion for the past 23 years. His diagnosis was delayed, as his symptoms and signs mimicked his underlying pulmonary diseases, such as emphysema and previous tuberculous pleurisy sequelae. A discrepancy was detected between the results of a ventilation-perfusion scan and the CT image. This was resolved by MRI, which showed retrograde blood flow from the right to the left pulmonary artery. Using MRI, we diagnosed this patient with isolated pulmonary artery hypoplasia and retrograde flow.

keywords
Pulmonary Artery, Hypoplasia, Magnetic Resonance Imaging, Regional Blood Flow

Reference

1.

1. Ten Harkel AD, Blom NA, Ottenkamp J. Isolated unilateral absence of a pulmonary artery: a case report and review of the literature. Chest 2002;122:1471-7.

2.

2. Bouros D, Pare P, Panagou P, Tsintiris K, Siafakas N. The varied manifestation of pulmonary artery agenesis in adulthood. Chest 1995;108:670-6.

3.

3. Rebergen SA, de Roos A. Congenital heart disease. Evaluation of anatomy and function by MRI. Herz 2000;25:365-83.

4.

4. Lynch DA, Higgins CB. MR imaging of unilateral pulmonary artery anomalies. J Comput Assist Tomogr 1990;14:187-91.

5.

5. Catala FJ, Martí-Bonmatí L, Morales-Marin P. Proximal absence of the right pulmonary artery in the adult: computed tomography and magnetic resonance findings. J Thorac Imaging 1993;8:244-7.

6.

6. Griffin N, Mansfield L, Redmond KC, Dusmet M, Goldstraw P, Mittal TK, et al. Imaging features of isolated unilateral pulmonary artery agenesis presenting in adulthood: a review of four cases. Clin Radiol 2007; 62:238-44.

7.

7. Massumi RA, Donohoe RF. Congenital absence versus acquired attenuation of one pulmonary artery. Circulation 1965;31:436-47.

8.

8. Raymond BA, Forsee JH. Acquired unilateral pulmonary artery hypoplasia. Surgery 1963;53:579-86.

9.

9. Rees RS, Somerville J, Underwood SR, Wright J, Firmin DN, Klipstein RH, et al. Magnetic resonance imaging of the pulmonary arteries and their systemic connections in pulmonary atresia: comparison with angiographic and surgical findings. Br Heart J 1987;58:621-6.

10.

10. Isawa T, Taplin GV. Unilateral pulmonary artery agenesis, stenosis, and hypoplasia. Radiology 1971;99:605- 12.

11.

11. Gluck MC, Moser KM. Pulmonary artery agenesis diagnosis with ventilation and perfusion scintiphotography. Circulation 1970;41:859-67.

12.

12. Steinberg I, Lyons HA. Ipsilateral hypoplasia of a pulmonary artery in advanced bronchiectasis. Am J Roentgenol Radium Ther Nucl Med 1967;101:939-46.

13.

13. Yacoub MH, Belcher JR, Attinson JN. Unilateral pulmonary artery hypoplasia associated with congenital cardiac anomalies. Br J Dis Chest 1965;59:102-12.

14.

14. Liebow AA, Hales MR, Lindskog GE. Enlargement of the bronchial arteries, and their anastomoses with the pulmonary arteries in bronchiectasis. Am J Pathol 1949; 25:211-31.

15.

15. Lin YM, Liang KW, Ting CT. Unilateral pulmonary artery agenesis with presentation of hemoptysis: a case report. Zhonghua Yi Xue Za Zhi (Taipei) 1999;62: 644-7.

Tuberculosis & Respiratory Diseases

e-Submission OA Policy