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Idiopathic Fibrosing Mediastinitis Causing Pulmonary Hypertension with Improvement by Steroid Treatment
서기현 (순천향대학교)
어수택 (순천향대학교)
김용훈 (순천향대학교)
김영통 (순천향대학교)
어성준 (순천향대)
박은서 (순천향대)
최재성 (순천향대)
오미혜 (순천향대)
나주옥
이상도
박춘식
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Abstract
Idiopathic fibrosing mediastinitis is, an uncommon cause of pulmonary hypertension this is characterized by excessive fibrosis of the mediastinum with an unknown etiology. Steroid therapy has been suggested for individuals with progressive symptoms, bu there is littlet data demonstrating the efficacy of such therapy are lacking. We present a case of pulmonary hypertension secondary to a compression of a main pulmonary artery by fibrosing mediastinitis which was confirmed by a biopsy with a thoracotomy. The chest CT scan and 2D echocardiography performed before and after a trial of steroid therapy demonstrated improvement after steroid therapy. (Tuberc Respir Dis 2006; 61: 74-79)
- keywords
- Fibrosing mediastinitis, Pulmonary hypertension, Steroid treatment., Fibrosing mediastinitis, Pulmonary hypertension, Steroid treatment.
참고문헌
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