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  • 한국과학기술정보연구원(KISTI) 서울분원 대회의실(별관 3층)
  • 2024년 07월 03일(수) 13:30
 

전종격동에서 발생한 악성 횡문근양 종양 1예

A Case of Malignant Rhabdoid Tumor in the Anterior Mediastinum

Tuberculosis & Respiratory Diseases / Tuberculosis & Respiratory Diseases,
2009, v.67 no.5, pp.462-466
오경진 (연세대학교)
이기병 (연세대학교)
홍순원 (연세대학교)
정교태 (연세대학교)
김형중 (연세대학교)
안철민 (연세대학교)
최홍규 (연세대학교)
장윤수 (연세대학교)
  • 다운로드 수
  • 조회수

Abstract

Malignant rhabdoid tumors arise primarily from the kidney. Extrarenal malignant rhabdoid tumors are rare, with the liver, central nervous system, and skin reported as the primary sites. Malignant rhabdoid tumors of the mediastinum are extremely rare among extrarenal malignant rhadoid tumors; only 3 cases have been reported to date, all characterized by aggressive clinical behavior. We experienced a 35-year-old woman diagnosed with malignant rhabdoid tumor in the anterior mediastinum with multiple metastases. The tumor was surgically unresectable, and treated with palliative radiation therapy. Three-month after radiation treatment, she died from dissemination of the malignant rabdoid tumor.

keywords
Rhabdoid Tumor, Mediastinum

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Tuberculosis & Respiratory Diseases