Abstract

When planning dental treatment for patients with rare diseases, a comprehensive evaluation of the patient's systemic condition, including oral examination, general growth, developmental stage, and medical history, is required. If the disease itself causes orofacial complications, it is essential for dentists to understand the disease and actively implement preoperative treatment to prevent complications such as infection and bleeding in col laboration with the primary physician. In addition, for patients who have difficulty with oral care due to a decline in intellectual ability and physical function, the role of the guardian and caregiver is important, and it is necessary to create a dental home environment. Patients with low compliance levels may consider dental treatment under general anesthesia and should receive continuous oral care, including dental adaptation training. Ultimately, it is essential to instruct patients and their guardians so that they can take care of their own oral health as they grow.