Abstract

Developmental dental rare diseases are conditions that affect the formation, development, and structure of teeth, often caused by genetic and environmental factors. These conditions can impact the shape, size, color, or number of teeth and, in severe cases, lead to functional and esthetic problems affecting oral health. Representative dis eases include dentinogenesis imperfecta, Amelogenesis imperfecta, oligodontia (hypodontia), regional odonto dysplasia, molar-incisor hypomineralization, and molar-incisor malformation. Medical and dental diagnoses, along with appropriate dental treatment and management, can alleviate symptoms and improve the quality of life for affected individuals. Orthodontic treatment, prosthetic rehabilitation, and surgical interventions may be required. Additionally, regular dental check-ups are essential during the growth period and beyond to ensure long-term management of these conditions