저자들은 폐렴을 동반한 기도의 드문 질환인 Mounier-Kuhn syndrome을 가진 환자의 단순흉부방사선, 기도내시경 소견과 함께 고식적인 흉부 전산화 단층 촬영을 시행 후 3차원적인 입체 영상으로 재구성한 소견을 고찰과 함께 1예 보고하는 바이다.
A 66-years-old man was refered to our hospital because of cough, sputum, chill and fever. Enlargement of the trachea and main bronchi on radiography and bronchoscopy is compatible with Mounier-Kuhn syndrome. Mounier-Kuhn syndrome or tracheobronchomegaly is a rare disorder of uncertain etiology, characterized by marked dilatation of the trachea and major bronchi. This syndrome is associated with tracheal diverticulosis, bronchiectasis and recurrent respiratory tract infection. We report a rare case of Mounier-Kuhn syndrome with pneumonia and literature reviews. (Tuberc Respir Dis 2006; 61: 403-406)
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