A Case of IgG4-Related Disease Presenting as Massive Pleural Effusion and Thrombophlebitis
민경훈 (고려대학교)
심재겸 (고려대학교)
오지연 (고려대학교)
이은주 (고려대학교)
허규영 (고려대학교)
이승헌 (고려대학교)
이승룡 (고려대학교)
김제형 (고려대학교)
이상엽 (고려대학교)
신철 (고려대학교)
심재정 (고려대학교)
인광호 (고려대학교)
강경호 (고려대학교)
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Abstract
Immunoglobulin (Ig) G4-related disease is a recently recognized systemic fibroinflammatory condition characterized by a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells with elevated circulating levels of IgG4. The disease can either be localized to one or two organs, or present as diffuse multi-organ disease. Furthermore, lesions in different organs can present simultaneously or metachronously. In the pulmonary manefestations, lesions associated with IgG4-related disease have been described in the lung parenchyma, airways and pleura, as well as the mediastinum. We report a case of IgG4-related disease presenting as massive pleural effusion and thrombophlebitis.
- keywords
- Immunoglobulin G, Pleural Effusion, Thrombophlebitis
참고문헌
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